Imaging of pulmonary manifestations in subtype B of Niemann-Pick disease.

Duchateau, F;Dechambre, S;Coche, Edgard
(2001) British Journal of Radiology — Vol. 74, n° 887, p. 1059-1061 (2001)

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Authors
  • Duchateau, FUCLouvain
    Author
  • Dechambre, SUCLouvain
    Author
  • Coche, EdgardUCLouvain
    Author
Abstract
We report the radiological and high resolution CT (HRCT) findings of the pulmonary involvement in a case of subtype B Niemann-Pick disease, diagnosed in an asymptomatic 22-year-old man, which was proved by bone marrow biopsy and sphingomyelinase assessment. In the present case, HRCT showed smooth interlobular septa thickening and a subtle ground-glass pattern.
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Citations

Duchateau, F., Dechambre, S., & Coche, E. (2001). Imaging of pulmonary manifestations in subtype B of Niemann-Pick disease. British Journal of Radiology, 74(887), 1059-1061. https://doi.org/10.1259/bjr.74.887.741059 (Original work published 2001)