We herein report the case of a 3-year-old girl with atypical congenital right upper limb lymphedema who developed an angiosarcoma. Only a few cases have been reported following congenital form of lymphedema and only 4 in such a young child. We also summarize all cases of angiosarcoma associated with congenital lymphedema reported in the literature.
Janssens, P., Dekeuleneer, V., Van Damme, A., Brouillard, P., Revencu, N., Clapuyt, P., Ferreira de Castro Moutinho, I., Ballieux, F., Vikkula, M., Marot, L., Baeck, M., & Boon, L. M. (2018). Angiosarcoma arising from congenital primary lymphedema. Pediatric Dermatology, 35(6), e382-e388. https://doi.org/10.1111/pde.13664 (Original work published 2018)