Unifocal and Multifocal Fibromuscular Dysplasia : Two Different Disease Entities in a Single Patient?

van Twist, Daan J.L.;de Leeuw, Peter W.;Spiering, Wilko;Rossi, Gian Paolo;Kroon, Abraham A.;et.al.
(2019) Hypertension — Vol. 73, n° 1, p. 7-12 (2019)

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Authors
  • van Twist, Daan J.L.
    Author
  • de Leeuw, Peter W.
    Author
  • Spiering, Wilko
    Author
  • Rossi, Gian Paolo
    Author
  • Author
  • Kroon, Abraham A.
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Abstract
(en) Fibromuscular dysplasia (FMD) is a heterogeneous group of nonatherosclerotic, noninflammatory vascular diseases that can be classified into 2 subtypes based on their angiographic appearance: the multifocal type, with its typical string-of-beads pattern, and the unifocal type, presenting as a single focal stenosis.1,2 Because these 2 FMD entities differ substantially with regard to clinical and histopathologic characteristics, it has been suggested that unifocal and multifocal FMDs in fact represent 2 different vascular diseases.3 Recently, however, we observed a patient in whom imaging studies suggest the coexistence of unifocal and multifocal FMD in a single patient. [...]
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Citations

van Twist, D. J. L., de Leeuw, P. W., Spiering, W., Rossi, G. P., Dominiczak, A. F., Jennings, G. L. R., Barigou, M., Persu, A., & Kroon, A. A. (2019). Unifocal and Multifocal Fibromuscular Dysplasia : Two Different Disease Entities in a Single Patient? Hypertension, 73(1), 7-12. https://doi.org/10.1161/hypertensionaha.118.12004 (Original work published 2019)