Portocaval fistulas are rare and only exceptionally discovered in newborns. We report the case of a large portocaval fistula associated with portal hypoperfusion detected at Doppler US imaging in an otherwise asymptomatic 5 week old infant. The patient remained asymptomatic over the following two years. At that time, preoperative angiogram showed a normal portal venous system and the fistula was surgically closed. Postoperative US showed a normal and patent portal system, without evidence of portal hypertension.
Nchimi, A., Khamis, J., Langhendries, J. P., Clapuyt, P., Saint Martin, C., Sokal, E., & Reding, R. (2001). Diagnostic et suivi d’une large fistule porto-cave intrahépatique chez un nouveau-né. Journal de radiologie, 82(11), 1642-1644. https://hdl.handle.net/2078.5/210167 (Original work published 2001)