Weight loss in a patient with polycystic kidney disease: when liver cysts are no longer innocent bystanders.
(2015) Acta Clinica Belgica — Vol. 70, n° 5, p. 369-371 (2015)
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- Abstract
- (en) OBJECTIVE AND IMPORTANCE: Autosomal dominant polycystic kidney disease (ADPKD) is the most frequent inherited kidney disorder, and liver involvement represents one of its major extra-renal manifestations. Although asymptomatic in most patients, polycystic liver disease (PLD) can lead to organ compression, severe disability and even become life-threatening, thereby warranting early recognition and appropriate management. CLINICAL PRESENTATION: We report the case of a 56-year-old woman with ADPKD and severe weight loss secondary to a giant hepatic cyst compressing the pylorus. Partial hepatectomy was required after failure of cyst aspiration and sclerotherapy, and patient's condition improved rapidly. DISCUSSION AND CONCLUSIONS: We discuss the presentation and classification of compressing liver cysts, and the available therapeutic alternatives for this potentially severe complication of ADPKD.
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Cecere, N., Hakem, S., Demoulin, N., Hubert, C., Jabbour, N., Goffette, P., Pirson, Y., & Morelle, J. (2015). Weight loss in a patient with polycystic kidney disease: when liver cysts are no longer innocent bystanders. Acta Clinica Belgica, 70(5), 369-371. https://doi.org/10.1179/2295333715Y.0000000024 (Original work published 2015)