Schnitzler syndrome associated with hairy cell leukemia presenting with chronic urticaria and arthralgias.
(2018) JAAD Case Reports — Vol. 4, n° 4, p. 386-389 (2018)
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- Authors
Tennstedt, Dominique 
- Abstract
- (en) Schnitzler syndrome is an underdiagnosed clinical condition characterized by 2 major criteria: chronic recurrent urticarial eruption and monoclonal IgM gammopathy, as well as at least 2 of the following minor criteria: (1) recurrent fever, (2) high C-reactive protein (CRP) levels, (3) signs of abnormal bone remodeling with or without bone pain, and (4) neutrophilic infiltrates on skin biopsy.1 We report the case of a patient with history of hairy cell leukemia who exhibited atypical clinical presentation of chronic urticaria for 2 years before the final diagnosis of Schnitzler syndrome was established. To the best of our knowledge, this is the first reported case of Schnitzler syndrome associated with hairy cell leukemia.
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Citations
Fank, H., Caers, J., Lambert, M., Marot, L., De Montjoye, L., Tennstedt, D., Baeck, M., & Dekeuleneer, V. (2018). Schnitzler syndrome associated with hairy cell leukemia presenting with chronic urticaria and arthralgias. JAAD Case Reports, 4(4), 386-389. https://doi.org/10.1016/j.jdcr.2017.12.012 (Original work published 2018)