Intérêt de la chirurgie de kystes pulmonaires liés à des dépôts de chaînes légères
(2020) Revue des Maladies Respiratoires — Vol. 37, n° 2, p. 180-186 (2020)
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- (en) [Effect of surgery of pulmonary cysts related to immunoglobulin light chain deposits] INTRODUCTION: Light chain deposition disease is a rare anatomo-clinical disorder, which rarely leads to cystic lung destruction. CASE REPORT: We report the case of a 62years old female patient with a history of a monoclonal gammopathy of unknown significance who developed progressive dyspnea. Thoracic CT-scan demonstrated a diffuse pulmonary cystic disorder with predominance in the right lower lobe. Thoracoscopic surgical resection of that lobe led to a diagnosis of non-amyloid kappa light chain deposits. Surgery also resulted in a lung volume reduction effect with clinical and functional benefits related to improved ventilation of adjacent segments. CONCLUSION: This report of pulmonary cystic disorder related to a light chain deposition disease highlights the potential clinical and functional benefits observed after lung volume reduction surgery.
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Delaey, P., Plawny, L., Nchimi, A., Hirschi, S., Weingertner, N., Santelmo, N., & Wirtz, G. (2020). Intérêt de la chirurgie de kystes pulmonaires liés à des dépôts de chaînes légères. Revue des Maladies Respiratoires, 37(2), 180-186. https://doi.org/10.1016/j.rmr.2020.01.001 (Original work published 2020)