Congenital etiologies of exocrine pancreatic insufficiency.

Scheers, Isabelle;Berardis, Silvia
(2022) Frontiers in Pediatrics — Vol. 10, p. 909925 [1-10] (2022)

Files

ScheersCongenitaletiologiespanreatic.pdf
  • Open Access
  • Adobe PDF
  • 739.33 KB
Download

Details

Authors
Abstract
Congenital exocrine pancreatic insufficiency is a rare condition. In a vast majority of patients, exocrine dysfunction occurs as part of a multisystemic disease, the most prevalent being cystic fibrosis and Shwachman-Bodian-Diamond syndrome. Recent fundamental studies have increased our understanding of the pathophysiology of these diseases. Exocrine pancreatic dysfunction should be considered in children with failure to thrive and fatty stools. Treatment is mainly supportive and consists of pancreatic enzyme replacement and liposoluble vitamins supplementation.
Affiliations

Citations

  • APA
  • Chicago
  • FWB

Scheers, I., & Berardis, S. (2022). Congenital etiologies of exocrine pancreatic insufficiency. Frontiers in Pediatrics, 10, 909925 [1-10]. https://doi.org/10.3389/fped.2022.909925 (Original work published 2022)