We report a new case of a right temporal pole variant of frontotemporal dementia (Rtv-FTLD), MD, who presented a slowly progressive deterioration of the recognition of familiar and famous people. We thoroughly investigated MD's face processing and semantic abilities, including a neuroimaging investigation. This analysis revealed a cross-modal person-based deficit together with a more general semantic alteration. However, there was no evidence of impairment in face perception, including holistic processing, or of an abnormal pattern of brain activation in face-sensitive cortical areas. We discuss the nature of face processing in the Rtv-FTLD and the context of a person-based semantic defect.
Busigny, T., Robaye, L., Dricot, L., & Rossion, B. (2009). Right anterior temporal lobe atrophy and Person-based semantic defect : a detailed case study. Neurocase, 15(6), 485-508. https://doi.org/10.1080/13554790902971141 (Original work published 2009)