Pulmonary arterial hypertension (PAH), associated with congenital heart disease (CHD), usually results from a systemic-to-pulmonary shunt. Eisenmenger syndrome (ES) is characterised by severe irreversible PAH and reversal of a previous systemic-to-pulmonary shunt. A national registry of ES patients was initiated to optimise patient care and to provide epidemiological information regarding PAH and CHD in Belgium.
Van de Bruaene, A., Delcroix, M., Pasquet, A., De Backer, J., De Pauw, M., Naeije, R., Vachiéry, J.-L., Paelinck, B., Morissens, M., & Budts, W. (2009). The Belgian Eisenmenger syndrome registry : implications for treatment strategies? Acta Cardiologica : an international journal of cardiology. https://doi.org/10.2143/AC.64.4.2041608