Hemangiomatosis of the spleen in a patient with Klippel-trénaunay syndrome.
(2013) Journal of the Belgian Society of Radiology — Vol. 96, n° 6, p. 357-359 (2013)
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- Authors
- Abstract
- Klippel-Trenaunay syndrome is a rare disorder characterized by a triad of port-wine stains, varicose veins, and bony and soft tissue hypertrophy usually involving an extremity. Visceral involvement in Klippel-Trénaunay syndrome is rare, but has been described in the colon, small bowel, bladder, kidney, spleen, liver, mediastinum and brain. In this paper we present the case of a 45-year-old woman with Klippel-Trenaunay syndrome in whom routine physical examination unexpectedly revealed the presence of a left upper quadrant mass. Abdominal US, contrast enhanced CT and whole-body PET-CT demonstrated multiple large cystic lesions within a massively enlarged spleen. Based on the clinical history and imaging findings diffuse hemangiomatosis of the spleen was suspected. This diagnosis was confirmed by pathologic examination after splenectomy.
- Affiliations
Ghent University Hospital Department of Pathology
Citations
Dekeyzer, S., Houthoofd, B., De Potter, A., Van Bockstal, M., Smeets, P., & Vogelaers, D. (2013). Hemangiomatosis of the spleen in a patient with Klippel-trénaunay syndrome. Journal of the Belgian Society of Radiology, 96(6), 357-359. https://doi.org/10.5334/jbr-btr.457 (Original work published 2013)